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Neonatal Med > Volume 18(1); 2011 > Article
Journal of the Korean Society of Neonatology 2011;18(1):117-123.
DOI: https://doi.org/10.5385/jksn.2011.18.1.117    Published online May 15, 2011.
A Clinical Study of Congenital Intrahepatic Portosystemic Shunt Diagnosed in Neonatal Period.
Ji Young Kim, Kyung A Kim, Yeon Kyung Lee, Sun Young Ko, Son Moon Shin, Byung Hee Han
1Department of Pediatrics, Cheil General Hospital, Kwandong University College of Medicine, Seoul, Korea. kkaped@hanmail.net
2Department of Radiology, Cheil General Hospital, Kwandong University College of Medicine, Seoul, Korea.
Congenital intrahepatic portosystemic shunts are rare disease and clinically asymptomatic shunts may be detected by chance on ultrasonogram before and after birth. We studied clinical course, treatment and prognosis of congenital intrahepatic portosystemic shunt at prenatal or neonatal period.
Medical records of 8 patients which were diagnosed in intrahepatic portosystemic shunt in Cheil General Hospital from 2006 through 2010 were reviewed retrospectively.
Eight patients with congenital intrahepatic portosystemic shunts were identified. Six patients were diagnosed at prenatal radiological screening, including three cases of intrauterine growth restriction and two cases of preterm baby. One case with increased serum ammonia underwent coil embolization. In four cases including one case that presented elevated direct bilirubin, shunts were closed spontaneously within 11th month after birth. Two patients were diagnosed on abdominal sonogram after birth because of elevated direct hyperbilirubinemia, all of whom presented intrauterine growth restriction. Closure of shunts was confirmed during 4th month to 6th month.
Congenital intrahepatic portosystemic shunts are clinically asymptomatic mostly and spontaneous closure is expected within 2 years age. But occasionally they have severe complication, so clinical and radiological observation is needed. Specially in cases of intrauterine growth retardation without evident cause, the possible diagnosis of congenital intrahepatic portosystemic shunts should be considered and prenatal and postnatal examination should be performed. When prenatal diagnosis is made, fetal wellbeing should be monitored periodically until spontaneous closure of shunts.
Key Words: Congenital intrahepatic portosystemic shunts; Intrauterine growth restriction


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