Congenital Intrahepatic Portosystemic Shunt in a Newbom Successfully Treated with Coil Embolization Via Umbilical Vein. |
Mi Jung Kang, Hong Keun Kim, Jung Sim Kim, Jung Mie Han, Sun Young Ko, Yong See Jun, Won Soon Park, Heung Jae Lee, Hye Kyung Yoon, Sung Wook Choo, Bo kyung Kim |
1Department of Pediatrics, College of Medicine, Sungkyunkwan University, Samsung Medical Center, Seoul, Korea. 2Department of Radiology, College of Medicine, Sungkyunkwan University, Samsung Medical Center, Seoul, Korea. |
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Abstract |
Congenital intrahepatic portosystemic shunt is a rare entity and is mostly reported in adults. In embryonic period, the vitelline vein is broken up into the vitelline sinusoids, which become the intrahepatic portal vein branches and the hepatic veins. The portosystemic venous shunts may develop from embryonic vascular remnants, including the vitelline vein and ductus venosus. We report for the first time in Korea a case of congenital intrahepatic portosystemic shunt in a newbom infant presenting with congestive heart failure and hepatomegaly, successfully treated by coil embolization via umbilical vein. |
Key Words:
Portosystenuc Shunt; Intrahepatic; Coil embolization; Neonate |
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