Two Cases of Pierre Robin Syndrome Managed with Tongue-Lip Adhesion and Tracheostomy.

Kim,  Shin Young; Lee,  Cho Ae; Kim,  Gye Sung; Han,  Man Yong; Kim,  Seo Jeong; Song,  Woo Shik; Kim,  Eun Seo; Lee,  Kyu Hyung

Case Report

Journal of the Korean Society of Neonatology 2002;9(1):122-127.
Published online May 1, 2002.

Two Cases of Pierre Robin Syndrome Managed with Tongue-Lip Adhesion and Tracheostomy.

Shin Young Kim, Cho Ae Lee, Gye Sung Kim, Man Yong Han, Seo Jeong Kim, Woo Shik Song, Eun Seo Kim, Kyu Hyung Lee

¹Department of Pediatrics, College of Medicine, Pochon CHA University, Sungnam, Korea. ksyped@hanmail.net
²Department of Oral and Maxillofacial Surgery, College of Medicine, Pochon CHA University, Sungnam, Korea.
³Department of Otorhinolaryngology-Head and Neck Surgery, College of Medicine, Pochon CHA University, Sungnam, Korea.

기관절개술과 혀-입술 유착술을 시행한 Pierre Robin 증후군 2례

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Abstract

Pierre Robin syndrome presents in the neonatal period with upper airway obstruction and feeding difficulties. Infants with pronounced micrognathia may fail to thrive because of chronic airway obstruction, or experience severe respiratory distress and feeding difficulties. This is potentially fatal and surgical intervention in these cases is necessary. We experienced two newborns with pronounced micrognathia who were managed with tongue-lip adhesion and tracheostomy. Herein, we report these two cases with literature reviews.

Key Words: Pierre Robin syndrome; Tongue-lip adhesion; Tracheostomy