A Case of Congenital Agenesis of the Gallbladder without Biliary Atresia associated with Duodenal Web.

Roh,  Eui Jung; Cho,  Eun Young; Lim,  Jae Woo; Cheon,  Eun Jung; Ko,  Kyoung Og; Mok,  Woo Kyun

Case Report

Journal of the Korean Society of Neonatology 2005;12(1):117-122.
Published online May 1, 2005.

A Case of Congenital Agenesis of the Gallbladder without Biliary Atresia associated with Duodenal Web.

Eui Jung Roh, Eun Young Cho, Jae Woo Lim, Eun Jung Cheon, Kyoung Og Ko, Woo Kyun Mok

¹Department of Pediatrics, College of Medicine, Konyang University, Daejeon, Korea. limsoa@hanmail.net
²Department of Pediatric Surgery, College of Medicine, Konyang University, Daejeon, Korea.

십이지장 격막과 동반된 담도 폐쇄 없는 담낭 무형성증 1례

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Abstract

Congenital absence of the gall bladder without extrahepatic biliary atresia is an extremely rare congenital malformation with a reported incidence ranging between 0.01 and 0.02%. It is thought to be occurred from failure of the gallbladder bud to develop in utero and frequent association with other malformations. Agenesis can be randomly discovered at autopsy or operations for symptoms suggestive of biliary tract disease. The authors report a case of agenesis of the gallbladder without extrahepatic biliary atresia in a neonate which was incidentally found at laparotomy for presumed duodenal obstruction, with a review of the literature.

Key Words: Agenesis of gallbladder; Extrahepatic biliary atresia; Duodenal obstruction